Disease Gerstmann - Straussler - Scheinker is a prion disease that causes muscle berkoordinasinya not accompanied by a slow deterioration of mental function . The disease is fatal , typically occurs about 5 years .
Such as Creutzfeldt-Jakob disease , Gerstmann - Straussler disease - Scheinker can occur anywhere in the world. Even so , this is not often the case than creutzfekdt - Jakob disease , begins early in life ( affects people in their 40s than in their 50s and 60s ) , and runs slower ( with an average life expectancy of 5 years up to 6 years ) .
Usually , the initial symptom is awkward and ill at ease when walking . Muscle spasms are more common than Creutzfeldt-Jakob disease . Talking becomes difficult , and forms of dementia . Nystagmus ( rapid movement of the eyes in one direction , followed by a slow return to the initial position ) , blindness , and deafness can occur . Loss of muscle coordination . Can vibrate and stiff muscles . normally , the muscles that control breathing and coughing becomes damaged , the result was a high risk of pneumonia , which generally leads to death.
Diagnosis
Diagnosis is determined by typical symptoms and a family history of the disease and can be confirmed by genetic testing . No treatment is available .
